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Three-Dimensional Printing of a Complex Aortic Anomaly
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Using 3D Heart Printing for Planning to Repair a Complex Congenital Heart Disease via Minimal Invasive Thoracotomy
Mohammed Abutaqa1, Hamza A Abdul-Hafez2, Hasan Alkhatib3
1Pediatric Cardiology Department, Palestinian Medical Complex, Ramallah, Palestine.
JACC. Case Reports
|June 27, 2025
Summary
Cor triatriatum sinister, a rare congenital heart defect, was successfully repaired using 3D printing for virtual surgical planning. This innovative approach enabled a precise, minimally invasive thoracotomy, improving patient outcomes.
Area of Science:
- Congenital Heart Surgery
- Cardiovascular Imaging
- 3D Printing in Medicine
Background:
- Cor triatriatum sinister is a rare congenital heart anomaly.
- It can present as left atrial obstructive lesions with varying symptoms.
- Diagnosis often involves echocardiography and CT scans.
Observation:
- A 14-year-old female presented with severe exercise intolerance.
- Echocardiography and CT revealed a fibromuscular membrane causing left atrial obstruction.
- Anomalous venous drainage with a persistent left superior vena cava to the coronary sinus was also noted.
Findings:
- Surgical intervention is the definitive treatment for cor triatriatum sinister.
- A 3D printed heart model was utilized for virtual surgical planning.
- This facilitated a safe and precise minimally invasive thoracotomy repair.
Implications:
- Minimally invasive approaches are feasible for complex congenital heart defects.
- 3D printing enhances surgical planning and precision.
- Multimodal imaging is crucial for improving surgical outcomes in rare cardiac conditions.
Keywords:
3D heart printingcongenital heart diseasecor triatriatum sinisterdouble superior vena cavaminimally invasive cardiac surgery
