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[Ostium primum and mitral cleft and aortic subvalvular stenosis. Apropos of 2 operated cases]
Insights
This study reports two rare pediatric cases of subaortic stenosis caused by a stenotic fibrous ring, a condition not found in existing literature. Surgical resection successfully relieved the obstruction in both children.
Area of Science:
- Pediatric Cardiology
- Congenital Heart Disease
- Cardiac Surgery
Background:
- Ostium primum defects are a type of congenital heart disease.
- Mitral clefts can be associated with various cardiac anomalies.
- Subaortic stenosis presents a significant obstruction to left ventricular outflow.
Abstract:
The two case reports are of children of 10 and 8 years of age with an ostium primum defect, with a mitral cleft and a stenotic fibrous ring below the aortic orifice. In the first case, the cause of the obstruction to left ventricular ejection was found at catheterisation, and in the second case it was an operative finding. In both cases there were large gradients, about 100 mmHg. The subaortic blockage was resected in both cases. A review of the literature has not revealed any similar case.