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Radiological Patterns of Pediatric Non-cystic Fibrosis Bronchiectasis: A Retrospective Study From Oman
Majid Al Jabri1, Ons Al Humaimi2, Fatma Al Yousufi2
1Child Health Department, Sultan Qaboos University Hospital, Muscat, OMN.
Non-cystic fibrosis bronchiectasis (NCFB) is often missed in children. High-resolution CT scans reveal diffuse patterns and specific types of bronchiectasis linked to conditions like primary immunodeficiency (PID) and primary ciliary dyskinesia (PCD).
Area of Science:
- Radiology
- Pediatric Pulmonology
- Medical Imaging
Background:
- Non-cystic fibrosis bronchiectasis (NCFB) is underdiagnosed in pediatric populations, especially in the Middle East.
- Early identification is crucial for managing pediatric respiratory conditions.
Purpose of the Study:
- To characterize high-resolution computed tomography (HRCT) features of NCFB in pediatric patients.
- To evaluate associations between HRCT findings and underlying clinical diagnoses in Oman.
Main Methods:
- Retrospective cross-sectional study at Sultan Qaboos University Hospital.
- Reviewed HRCT reports of pediatric patients (≤18 years) diagnosed with NCFB.
- Analyzed clinical features, radiological patterns, lobar involvement, and etiologies.
Main Results:
- 61 pediatric patients with NCFB were analyzed; mean age at diagnosis was 7.3 years.
- Diffuse bronchiectasis (78.7%) was predominant, frequently involving multiple lobes.
- Cylindrical bronchiectasis was universal; cystic and varicose forms were more common in systemic disorders like PID and PCD.
Conclusions:
- HRCT is vital for diagnosing pediatric NCFB, especially in children with recurrent infections or comorbidities.
- Early imaging can prevent irreversible lung damage and guide treatment.
- National guidelines and multidisciplinary assessments can improve diagnostic timeliness and outcomes.
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