Langerhans cell histiocytosis disguised as lichenoid eruption

Langerhans cell histiocytosis (LCH) is an inflammatory clonal proliferative neoplasm of immature myeloid precursor cells. These cells can accumulate in various tissues including skin, leading to tissue damage, and in some cases organ dysfunction. Herein, a report of a 1-year-old girl who presented with multiple lichenoid pinkish to purplish flat-topped papules, some of them were crusted and linear over the trunk mimicking lichen planus. The histopathologic and immunohistochemical staining confirmed the diagnosis of LCH. Awareness about this rare entity is important for early detection, timely intervention, and effective management.