The PKU Patient Registry: Development of a patient-driven registry and initial outcomes

Lauren Youngborg1, Christine S Brown1, Eileen M Blakely1

  • 1National PKU Alliance, Roanoke, VA, USA.

PubMed

Insights

The PKU Patient Registry collects patient-entered data on lived experiences and health for phenylketonuria (PKU). This valuable resource supports research and aids in recruiting participants for studies, improving understanding of the condition.

Area of Science:

  • Patient-reported outcomes
  • Rare disease registries
  • Phenylketonuria (PKU) research

Background:

  • Patient registries are crucial for collecting data on specific conditions.
  • Patient-entered registries prioritize patient and family perspectives.
  • The National PKU Alliance (NPKUA) established a registry to support phenylketonuria (PKU) research.

Purpose of the Study:

  • To collect patient-entered lived experience and natural history data for PKU.
  • To gather insights into the needs of the PKU community.
  • To facilitate recruitment for external research studies.

Main Methods:

  • The PKU Patient Registry was launched in 2017 by NPKUA.
  • It utilizes the IAMRARE® platform for secure data collection.
  • Surveys include validated tools and patient-reported outcomes developed with stakeholders.

Main Results:

  • As of November 2024, 1125 participants from 46 states and 36 countries are enrolled.
  • Over 123,000 surveys have been completed.
  • The registry has supported over 35 external research studies and shared anonymized data.

Conclusions:

  • The PKU Patient Registry provides longitudinal, patient-entered data.
  • It enhances understanding of PKU's natural history.
  • The registry facilitates collaboration and improves research recruitment.

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