Sphenopharyngeal encephalocele associated with agenesis of the corpus callosum

A case of a 38-year-old patient, who had been complaining for some years about impairment in nasal breathing, is presented. Within the last few months the patient presented a rapid deterioration of his visual acuity. Radiological examinations revealed a sphenopharyngeal encephalocele as well as agenesis of corpus callosum. The pathogenesis and therapy of the disease is discussed in the light of the particular case presented as well as those cases reported in the literature.