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Partial AVSD with cortriatriatum sinister with unroofed coronary sinus in an adult

Amitabh Satsangi1, Sheikh Mohd Murtaza1

  • 1Department of Cardiothoracic and Vascular Surgery, All India Institute of Medical Sciences, New Delhi, India.

Annals of Pediatric Cardiology
|August 15, 2025
PubMed

Insights

This study reports a rare case of partial atrioventricular septal defect (AVSD) with cor triatriatum sinister (CTS) in an adult. Surgical management was successful, highlighting the need for thorough preoperative imaging in AVSD cases.

Area of Science:

  • Cardiology
  • Congenital Heart Disease
  • Surgical Management

Background:

  • Atrioventricular septal defect (AVSD) and cor triatriatum sinister (CTS) are rare congenital heart anomalies.
  • Combined AVSD and CTS is exceptionally uncommon, with few documented cases.
  • Isolated CTS with partial AVSD, left superior vena cava, and unroofed coronary sinus in adults remains unreported.

Observation:

  • A 20-year-old male with known partial AVSD and CTS presented with exertional dyspnea.
  • The patient underwent surgical correction.
  • The postoperative course was uneventful.

Findings:

  • This case represents the first reported instance of isolated CTS with partial AVSD, left superior vena cava, and unroofed coronary sinus in an adult.
  • Successful surgical intervention was achieved.
  • The patient experienced a favorable recovery.

Implications:

  • Comprehensive preoperative imaging is crucial for identifying all associated cardiac lesions in patients with AVSD.
  • Early diagnosis and surgical intervention can lead to positive outcomes in complex congenital heart defects.
  • This case expands the understanding of rare congenital heart anomaly combinations and their management.

Keywords:
Adult congenital heart diseaseatrioventricular septal defectcor triatriumunroofed coronary sinus

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