Mind the right ventricle: Tackling right heart dysfunction in left ventricular diverticulum with omphalocele

Left ventricular diverticulum (LVD) is a rare congenital anomaly characterized by an abnormal outpouching of the left ventricular wall. It is often identified during childhood, as it is commonly associated with midline thoracoabdominal defects and other congenital heart abnormalities. Here, we present a 10-month-old boy with a LVD and omphalocele posted for surgical management who had difficulty weaning in the post-operative period. We discuss the unique challenges that necessitate meticulous planning and execution to optimize right ventricular function and prevent pulmonary arterial hypertension in such patients.