Mind the right ventricle: Tackling right heart dysfunction in left ventricular diverticulum with omphalocele

Pavana Gokhale1, Tanya Mital1, Pradeep R Reddy2

  • 1Department of Cardiac Anaesthesia and Critical Care, Cardiothoracic and Neurosciences Centre, All India Institute of Medical Sciences, New Delhi, India.

Insights

A rare congenital heart defect, left ventricular diverticulum (LVD), can complicate surgical recovery in infants. Careful management is key to optimizing heart function and preventing pulmonary hypertension post-surgery.

Area of Science:

  • Cardiology
  • Pediatric Surgery
  • Congenital Heart Disease

Background:

  • Left ventricular diverticulum (LVD) is a rare congenital anomaly involving abnormal outpouching of the left ventricular wall.
  • LVD is frequently diagnosed in childhood and often co-occurs with midline thoracoabdominal defects and other congenital heart abnormalities.

Observation:

  • This report details a 10-month-old boy diagnosed with LVD and omphalocele requiring surgical intervention.
  • The patient experienced significant challenges with post-operative weaning.

Findings:

  • The case highlights the complex management of pediatric patients with combined LVD and omphalocele.
  • Specific attention is required to optimize right ventricular function and mitigate the risk of pulmonary arterial hypertension.

Implications:

  • Meticulous surgical planning and execution are crucial for successful outcomes in these complex cases.
  • Early identification and management strategies are essential for improving the prognosis of infants with LVD and associated anomalies.

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