Arrhythmogenic Cardiomyopathy with Biventricular Involvement and Right Ventricular Thrombosis: A Multi-modality

Fawaz Bardooli1, Dhuha Rashed Aljawder1, Dileep Kumar2

  • 1Mohammed Bin Khalifa Specialist Cardiac Centre, Awali, Bahrain, UAE.

Insights

Arrhythmogenic cardiomyopathy (AC) is an inherited heart condition causing fibro-fatty ventricular changes. This case highlights AC with biventricular involvement, right ventricular thrombosis, and left bundle branch block ventricular tachycardia.

Area of Science:

  • Cardiology
  • Genetics
  • Medical Imaging

Background:

  • Arrhythmogenic cardiomyopathy (AC) is an inherited cardiac disorder.
  • It involves fibro-fatty replacement of ventricular tissue.
  • AC can manifest as ventricular tachycardia (VT), often with left bundle branch block (LBBB) morphology.

Observation:

  • This report details a patient with LBBB VT.
  • Multi-modality imaging revealed AC with biventricular involvement.
  • Right ventricular (RV) thrombosis was also identified.

Findings:

  • Cardiovascular magnetic resonance (CMR) is crucial for diagnosing AC.
  • The patient presented with biventricular AC and RV thrombus.
  • Treatment included antiarrhythmics, heart failure management, and ICD implantation.

Implications:

  • This case underscores the importance of comprehensive imaging in AC diagnosis.
  • Management involves addressing both the arrhythmia and thromboembolic risk.
  • Successful treatment strategies for complex AC presentations are demonstrated.

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