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Updated: Sep 9, 2025

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Severe Oral Lichen Planus Masking a Primary Immunodeficiency: X-Linked Lymphoproliferative Disease Type 1 (XLP-1)

Magí Brufau-Cochs1, Ángela Deya Martínez2,3,4,5, Mariana Álvarez Vukov6

  • 1Department of Dermatology, Hospital Sant Joan de Déu, Barcelona, Spain.

Pediatric Dermatology
|September 4, 2025
PubMed

Keywords:
SH2D1AXLP‐1X‐linked lymphoproliferative diseasegeneticsoral mucous lesionsprimary immunodeficiencies

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