First Reported Case of Intracardiac Kimura Disease.
Andrew D Wisneski1, Jamal S Rana2, Eugene Fan3
1Division of Cardiothoracic Surgery, Department of Surgery, University of California San Francisco, San Francisco, California, USA.
JACC. Case Reports
|September 6, 2025
Summary
This report details the first intracardiac Kimura disease case, a rare inflammatory condition. Surgical resection of the heart mass was successful, with no recurrence observed during follow-up.
Area of Science:
- Cardiology
- Pathology
- Rare Diseases
Background:
- Kimura disease is a rare inflammatory condition typically affecting the head and neck with subcutaneous nodules.
- Intracardiac involvement of Kimura disease is exceptionally rare, with no prior documented cases.
- This case presents the first instance of Kimura disease manifesting within the heart.
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