Re-do VATS for recurrent pneumothorax in a Birt-Hogg-Dubé syndrome patient

Birt-Hogg-Dubé syndrome (BHDS) is an autosomal dominant inherited disorder caused by mutation in a tumour suppressor gene, FLCN, leading to skin tumours (fibrofolliculomas), renal tumours and pulmonary cysts. Lung involvement is predominantly observed in 70% of the cases of BHDS, manifesting in the form of recurrent primary spontaneous pneumothorax. This video tutorial showcases the surgical management of recurrent right primary spontaneous pneumothorax in a young adult with a history of multiple episodes of bilateral pneumothorax managed by surgical intervention previously. The study underscores the efficacy of video-assisted thoracic surgery surgical management coupled with talc pleurodesis in restoring incomplete pleural symphysis in BHDS patients, as evident from successful surgery and uneventful recovery of the patient.