[Autosomal recessive albopapuloid dystrophic epidermolysis bullosa]

Albopapules are usually considered as pathognomonic lesions of Pasini's epidermolysis bullosa, which is dominantly transmitted. Herein, we are reporting 3 cases of recessively inherited epidermolysis bullosa with albopapules. The clinical, histological and ultrastructural features are described. It is concluded that the presence of albopapules is not necessarily a safe criterion for the diagnosis of Pasini's epidermolysis bullosa.