[The glaucoma of encephalo-trigeminal angiomatoses]

A study of 9 cases of trigeminal noevus flammeus was performed. Eight had congenital glaucoma and where followed from 1 to 10 years. Only three had intracranial involvement. Hemangiomatosis was often atypical: including cavernous hemangioma, association with cutis marmorata telangiectatica congenital and bilateral involvement. Glaucoma was a mild congenital glaucoma in all cases improved by surgical treatment. Surgery was easily performed and a superficial capillary network on the sclera was seen in all patients. No genetic factor was demonstrated in our patients.