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Respiratory Involvement During the Course of Hypocomplementemic Urticarial Vasculitis: A Case Report
Leroy Dorian1, Rudi Peché2, Julien Guiot3
1Pulmonary Medicine, Université Libre de Bruxelles, Brussels, BEL.
Hypocomplementemic urticarial vasculitis syndrome can cause severe lung damage, even in young, non-smoking patients. Early diagnosis and appropriate treatment are crucial to prevent irreversible respiratory complications in this rare condition.
Area of Science:
- Rheumatology
- Pulmonology
- Dermatology
Background:
- Hypocomplementemic urticarial vasculitis syndrome (HUVS) is a rare small-vessel vasculitis.
- It presents with chronic urticaria and vasculitis, often mimicking systemic lupus erythematosus (SLE).
- The hypocomplementemic form has a more severe prognosis, particularly with respiratory involvement.
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