Chronic kidney disease- mineral and bone disorder in autosomal dominant policystic kidney disease
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Updated: Jan 17, 2026

Use of Ultra-high Field MRI in Small Rodent Models of Polycystic Kidney Disease for In Vivo Phenotyping and Drug Monitoring
Published on: June 23, 2015
S Lai1, A M Perrotta1, L Tartaglione1
1Department of Translational and Precision Medicine, Nephrology Unit, Sapienza University of Rome, Rome, Italy.
Insights
Autosomal dominant polycystic kidney disease (ADPKD) involves unique mineral and bone disorders, including elevated FGF23 and low bone turnover, even in early chronic kidney disease (CKD) stages. These conditions stem from kidney cysts and Polycystin disruptions, necessitating targeted management.
Area of Science:
- Nephrology
- Endocrinology
- Bone Biology
Background:
- Autosomal dominant polycystic kidney disease (ADPKD) is the leading genetic kidney disorder, causing progressive renal function loss.
- ADPKD patients exhibit unique mineral and bone disorder patterns distinct from general chronic kidney disease (CKD).
Purpose of the Study:
- To review the distinct mineral and bone disorders in early-stage ADPKD.
- To highlight the role of FGF23 and Polycystin signaling in ADPKD-related bone complications.
Main Methods:
- Literature review focusing on mineral and bone disorders in ADPKD.
- Analysis of the impact of cystic tissues on FGF23 production.
- Examination of Polycystin-1 and Polycystin-2 roles in bone metabolism.
Main Results:
- Elevated circulating FGF23 levels due to extraosseous production by kidney and liver cysts in ADPKD.
- Increased prevalence of low bone turnover disease in ADPKD compared to other CKD forms.
- Disrupted Polycystin signaling in osteocytes/osteoblasts impairs bone anabolism.
Conclusions:
- ADPKD-associated mineral and bone disorders require comprehensive monitoring and management.
- Early intervention and targeted therapies are crucial for mitigating disease progression and improving outcomes in ADPKD patients.
Abstract:
Autosomal dominant polycystic kidney disease (ADPKD) is the most common genetic disorder characterized by bilateral renal cysts that detach from parental tubules, progressively leading to renal function loss. Patients with ADPKD represent a unique subset of chronic kidney disease (CKD) individuals, sharing common CKD features while also exhibiting distinct traits specific to ADPKD. This review described the unique patterns of mineral and bone disorders present in ADPKD in the early CKD stages. The principal points are: the extraosseous FGF23 production by cystic tissues in the kidneys and liver, resulting in elevated circulating FGF23 levels with possible impact on calcium and phosphate balance and cardiovascular risk in ADPKD; the higher prevalence of low bone turnover disease in ADPKD than in other forms of CKD. This is likely due to disruptions in signals mediated by the Polycystin-1 and Polycystin-2 heterodimers, which are expressed on the primary cilia of osteocytes and osteoblasts, leading to impaired bone anabolism. Given these insights, a comprehensive approach is essential for monitoring and managing mineral and bone disorders in ADPKD patients. Early intervention and targeted therapies could mitigate the progression of mineral and bone disorders and possibly improve patient outcomes.
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