Arrhythmogenic Cardiomyopathy and Biomarkers: A Promising Perspective?
Federico Barocelli1, Nicolò Pasini1, Alberto Bettella1
1Cardiology Division, Parma University Hospital, 43126 Parma, Italy.
Insights
Biomarkers show promise for diagnosing arrhythmogenic cardiomyopathy (ACM), a heart muscle disease. Integrating these markers with imaging and genetics may improve early detection and personalized treatment.
Area of Science:
- Cardiology
- Genetics
- Biomarker Discovery
Background:
- Arrhythmogenic cardiomyopathy (ACM) is a genetic heart muscle disease causing myocardial fibrosis, arrhythmias, and sudden cardiac death.
- Early ACM diagnosis is difficult due to incomplete penetrance and variable expressivity, with fatal events often occurring early.
- Reliable biomarkers are needed to improve diagnostic accuracy, risk stratification, and clinical management of ACM.
Purpose of the Study:
- To review current and emerging biomarkers for arrhythmogenic cardiomyopathy (ACM).
- To assess the potential role of biomarkers in enhancing ACM diagnosis and management.
- To explore the integration of biomarkers with other diagnostic modalities.
Main Methods:
- Narrative review of scientific literature on ACM biomarkers.
- Examination of various biomarker categories: troponins, natriuretic peptides, inflammatory proteins, microRNAs, fibrosis markers.
- Discussion of genetic testing and cardiac imaging in ACM diagnosis.
Main Results:
- Several biomarkers are associated with ACM severity, arrhythmic burden, and disease progression.
- Current biomarkers have limited routine clinical utility as standalone diagnostic tools.
- Multimodal diagnostic strategies combining biomarkers, imaging, and genetics show promise.
Conclusions:
- No single biomarker is sufficient for standalone ACM diagnosis.
- Ongoing research in multi-marker panels and novel targets offers future potential.
- Integrating circulating biomarkers with imaging, genetic, and clinical data may improve early ACM detection and personalized therapy.
Abstract:
Arrhythmogenic cardiomyopathy (ACM; MIM #107970) is a primitive heart muscle disease characterized by progressive myocardial loss and fibrosis or fibrofatty replacement, predisposing patients to ventricular arrhythmias, sudden cardiac death, and heart failure. Despite advances in imaging and genetics, early diagnosis remains challenging due to incomplete penetrance, variable phenotypic expressivity, and the fact that fatal arrhythmic events may often occur in the early stages of the disease. In this context, the identification of reliable biomarkers could enhance diagnostic accuracy, support risk stratification, and guide clinical management. This narrative review examines the current landscape of potential and emerging biomarkers in ACM, including troponins, natriuretic peptides, inflammatory proteins, microRNAs, fibrosis-related markers, and other molecules. Several of these biomarkers have demonstrated associations with disease severity, arrhythmic burden, or structural progression, although their routine clinical utility remains limited. The increasing relevance of genetic testing and non-invasive tissue characterization-particularly through cardiac imaging techniques-should also be emphasized as part of a multimodal diagnostic strategy in which biomarkers may play a complementary role. Although no single biomarker currently meets the criteria for a standalone diagnostic application, ongoing research into multi-marker panels and novel molecular targets offers promising perspectives. In conclusion, the integration of circulating biomarkers with imaging findings, genetic data, and clinical parameters may open new avenues for improving early detection and supporting personalized therapeutic strategies in patients with suspected ACM.
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