From Fetal Diagnosis to Staged Percutaneous Palliation: A Case of Double Right-Valve Dysplasia

Tricuspid valve dysplasia (TVD) and pulmonary valve dysplasia (PVD) are rare congenital anomalies that challenge prenatal counseling and postnatal care. When feasible, biventricular repair is the highest priority choice.

We report a prenatal diagnosis of non-Ebstein TVD with severe regurgitation, hypoplastic right ventricle (RV), and PVD with an intact ventricular septum. Prenatal counseling illustrated the potential ventricular repair plan. During the postnatal period, pulmonary valvuloplasty was performed, followed by stenting of the ductus arteriosus. The patient demonstrated clinical improvement, a progressive increase in RV size, and satisfactory pulmonary flow over time.

This case highlights the significance of early intervention in facilitating RV growth and maximizing biventricular circulation. The literature describes staged catheter-based approaches as therapies that can avoid univentricular palliation.

Prenatal diagnosis of TVD with PVD enables timely planning and early biventricular repair, promising better long-term outcomes. A staged, personalized approach can promote RV growth.