Transitioning care in cystic fibrosis: a comprehensive review of reviews of clinical and psychosocial outcomes
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Summary
This summary is machine-generated.Structured transition models improve care for cystic fibrosis (CF) patients. Joint clinics and readiness tools enhance self-management and adherence, ensuring better continuity of care for adolescents and young adults with CF.
Area Of Science
- Healthcare Management
- Patient Transition Care
- Systematic Review Synthesis
Background
- Rising life expectancy in cystic fibrosis (CF) necessitates effective transition from pediatric to adult care.
- Structured transition models aim to enhance care continuity, clinical stability, and psychosocial outcomes.
- This review synthesizes evidence on the effectiveness of transition models across healthcare systems.
Purpose Of The Study
- To systematically review evidence on the effectiveness of structured transition models for cystic fibrosis patients.
- To compare the impact of different structured transition interventions on clinical and psychosocial outcomes.
- To identify best practices for transitioning CF patients from pediatric to adult care.
Main Methods
- Searched for systematic reviews and reviews published between 2005 and 2025.
- Assessed methodological quality using AMSTAR 2 and quantified study overlap with CCA.
- Conducted a narrative synthesis of included reviews, stratified by intervention type and geography.
Main Results
- Structured programs were more effective than informal approaches.
- Joint pediatric-adult clinics preserved lung function and reduced hospitalizations.
- Readiness tools improved self-management; transition coordinators enhanced adherence and satisfaction.
Conclusions
- Structured transition models, especially joint clinics and coordinator-led care, improve self-management, adherence, and care continuity for CF patients.
- Further systematic reviews should investigate the long-term clinical outcomes of these models.
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