Dental Management of a Child With Temtamy Syndrome: A Case Report

Temtamy syndrome is a rare genetic disorder that follows an autosomal recessive pattern. It is characterized by intellectual disability, developmental delays, and distinctive facial features. It may also affect the eyes, heart, and skeletal system. This case report details the dental treatment of a four-year-old male patient recently diagnosed with Temtamy syndrome. The patient complained of dental pain and presented with generalized developmental delay, intellectual disability, and hypotonia. Full dental rehabilitation under general anesthesia was planned due to behavior issues. Micrognathia and a limited mouth opening were among the challenges faced during the dental treatment. A limited mouth opening can be managed under general anesthesia, but if the child were to be treated under local anesthesia, this would further complicate the treatment. Therefore, the recommended treatment option when treating such patients is under general anesthesia to overcome these problems. This case report aims to discuss the oral features and dental management of children with Temtamy syndrome, which will aid fellow dentists in anticipating challenges faced in such cases, and further, understand the disease.