Giant Cell Arteritis Causing Isolated Pulmonary Artery Aneurysm.
Ivka R Stimach1, Adil F Vural2, Marissa Edmiston3
1Department of Internal Medicine, MetroHealth Medical Center/Case Western Reserve University, Cleveland, Ohio, USA.
JACC. Case Reports
|December 11, 2025
Summary
Pulmonary artery aneurysms (PAA) are rare. This case details a PAA caused by giant cell arteritis, a rare autoimmune vasculitis, successfully treated with surgery, highlighting an unusual etiology and treatment approach.
Area of Science:
- Cardiovascular Medicine
- Rheumatology
- Vascular Surgery
Background:
- Pulmonary artery aneurysms (PAA) are rare, with an incidence of approximately 1 in 14,000.
- Etiologies for PAA are diverse, including malignancy, infection, congenital conditions, autoimmune diseases, and vasculitis.
- Giant cell arteritis (GCA) is an uncommon cause of PAA, typically affecting large and medium-sized vessels.
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