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Multifocal Spinal Intradural Myxopapillary Ependymoma
Rahul S Agrawal1, Siddharth Aiyer1, Ajay Kothari1
1Sancheti Institute for Orthopaedics & Rehabilitation, Pune, India.
Indian Journal of Orthopaedics
|December 15, 2025
Summary
This case study highlights a rare multifocal myxopapillary ependymoma (MPE) in a young adult. Despite initial successful surgery, the patient experienced recurrence and metastasis, necessitating whole-spine irradiation.
Area of Science:
- Neuro-oncology
- Spinal Cord Tumors
- Neuropathology
Background:
- Myxopapillary ependymomas (MPEs) are rare WHO grade II spinal tumors, accounting for about 15% of spinal ependymomas.
- Multifocal MPE presentation at initial diagnosis in adults is exceptionally rare, with limited literature.
- MPEs, despite a generally favorable prognosis, carry a high risk of recurrence, underscoring the need for vigilant long-term monitoring.

