Sudden Death in a Child Revealing a Multifocal Cardiac Fibroma: A Hidden Lethal Threat
View abstract on PubMed
Summary
This summary is machine-generated.A rare multifocal cardiac fibroma caused sudden death in a child. This case highlights the silent, lethal potential of these benign heart tumors and the need for early detection in pediatric populations.
Area Of Science
- Pediatric Cardiology
- Cardiac Pathology
- Oncology
Background
- Cardiac fibromas, despite benign histology, pose significant risks including arrhythmias and sudden death.
- Pediatric cardiac tumors are rare but can have severe consequences.
Purpose Of The Study
- To report a rare case of multifocal cardiac fibroma presenting as sudden death in a child.
- To emphasize the importance of recognizing silent cardiac tumors in pediatric patients.
Main Methods
- Autopsy and detailed histologic examination of the heart.
- Description of the tumor's size, location, and microscopic features.
Main Results
- A four-year-old boy experienced sudden death, with autopsy revealing a large multifocal cardiac fibroma in the left ventricle.
- Histology confirmed spindle cell proliferation consistent with cardiac fibroma, with no signs of atypia or necrosis.
Conclusions
- Multifocal cardiac fibromas are exceptionally rare and can be fatal if undiagnosed.
- Increased awareness and early cardiac imaging are crucial for preventing sudden death from pediatric cardiac tumors.
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