Total hip replacement in Klippel-Trenaunay syndrome with massive AV Malformations. A Case report

KTS, known as Klippel-Trenaunay syndrome, is a rare condition present at birth that includes a combination of capillary malformation, varicose veins, or venous malformation in the lower limbs, and excessive growth of bone and soft tissue.

This report describes a female patient has 53-year-old suffering from Klippel-Trenaunay syndrome with arteriovenous malformations who underwent total hip arthroplasty surgery. The treatment included preoperative embolization, intraoperative angiography to place an iliac artery occlusive balloon, and the use of modular hip arthroplasty components to address femoral and acetabular dysplasia.

In the case of patients with the syndrome (KT), all problems that the patient suffers from must be discussed with a team of specialists and experienced people, and they also, require a radiologic evaluation for malformations to determine the most suitable surgical approach and make the right decision about whether to operate or not, avoid failure, and obtain the best results.