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Published on: July 18, 2014
HRS/ISACHD/PACES scientific statement on provider and institutional best practices for comprehensive adult congenital
Paul Khairy1, Susan P Etheridge2, John Jairo Araujo3
1Electrophysiology Service and Adult Congenital Center, Montreal Heart Institute, Université de Montréal, Montreal, Canada.
Insights
Adults with congenital heart disease (ACHD) face increasing arrhythmia risks. This statement establishes ACHD electrophysiology as a subspecialty, defining best practices for comprehensive care and training to improve outcomes.
Area of Science:
- Cardiology
- Electrophysiology
- Adult Congenital Heart Disease
Background:
- The global population of adults with congenital heart disease (ACHD) now exceeds that of children.
- Arrhythmias are a leading cause of morbidity, hospitalization, and mortality in this aging population.
- ACHD arrhythmia mechanisms are complex, stemming from congenital defects, surgical alterations, and acquired risk factors.
Purpose of the Study:
- To define best practices for comprehensive ACHD electrophysiology programs.
- To establish ACHD electrophysiology as a distinct subspecialty.
- To propose a competency-based framework for ACHD electrophysiology care.
Main Methods:
- A joint statement from leading professional societies (HRS, PACES, ISACHD).
- Development of a competency-based framework across five key domains.
- Outlining requirements for pre-procedural evaluation, procedural planning, and peri/post-procedural management.
- Specification of institutional requirements for personnel, facilities, and infrastructure.
Main Results:
- Establishes ACHD electrophysiology as a distinct subspecialty.
- Proposes a competency framework covering anatomy, arrhythmia mechanisms, assessment, procedures, and longitudinal care.
- Defines best practices for provider and center-level care.
- Suggests candidate performance metrics for efficacy, safety, outcomes, and patient-reported status.
Conclusions:
- Recommendations aim to standardize and improve ACHD arrhythmia care.
- Promotes the development of regional centers of excellence and harmonized training.
- Aims to ensure safe, effective, and equitable care for adults with congenital heart disease and arrhythmias.
Abstract:
The global population of adults with congenital heart disease (CHD) now exceeds that of children, reflecting decades of surgical and medical advances. As this cohort has aged, arrhythmias have emerged as a predominant cause of morbidity, hospitalization, and late mortality. Arrhythmia mechanisms in adult CHD (ACHD) arise from congenital abnormalities, surgically altered substrates, progressive hemodynamic lesions, multisystem comorbidities, and acquired cardiovascular risk factors, creating a distinct electrophysiological (EP) phenotype that diverges fundamentally from that of populations without CHD. Despite increasing complexity and demand, ACHD EP care remains fragmented, with marked variability in provider training, institutional resources, and access to specialized expertise. This joint Heart Rhythm Society/Pediatric and Congenital Electrophysiology Society/International Society for Adult Congenital Heart Disease statement defines provider- and center-level best practices for comprehensive ACHD EP programs. It establishes ACHD EP as a distinct subspecialty and proposes a competency-based framework spanning 5 domains: congenital cardiac anatomy and physiology, arrhythmia mechanisms and risk stratification, noninvasive EP assessment, procedural proficiency in ablation and device therapy, and longitudinal ACHD arrhythmia care. The statement outlines key elements of preprocedural evaluation, procedural planning, and peri- and postprocedural management and specifies institutional requirements for personnel, facilities, and infrastructure. Recognizing the paucity of validated ACHD-specific performance metrics, the document proposes candidate indicators of procedural efficacy, safety, efficiency, longitudinal outcomes, and patient-reported health status and articulates principles for credentialing and institutional accountability. These recommendations are intended as scalable standards to support regional centers of excellence and harmonized training pathways, thereby promoting safe, effective, and equitable ACHD arrhythmia care.
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