2025 Clinical Practice Guidelines for the Management of Fontan Patients in Korea: A Consensus Statement With Graded

Min-Jung Cho1, Soo In Jeong2, Soo-Jin Kim3

  • 1Department of Pediatrics, Gyeongsang National University Changwon Hospital, Changwon, Korea.

Korean Circulation Journal
|February 19, 2026
PubMed

Insights

Korean pediatric cardiology has improved complex congenital heart disease outcomes. New clinical practice guidelines offer tailored long-term management for Fontan circulation patients in Korea.

Area of Science:

  • Pediatric Cardiology
  • Congenital Heart Disease
  • Cardiovascular Surgery

Background:

  • Significant advances in pediatric cardiology over 4 decades have improved prognosis for complex congenital heart diseases, including single ventricle physiology.
  • An increasing number of patients with congenital heart disease are reaching adulthood, necessitating updated long-term management strategies.
  • There is a specific need for clinical practice guidelines reflecting current medical trends for Fontan circulation patients.

Purpose of the Study:

  • To establish the first Korean clinical practice guidelines for the long-term management of Fontan patients.
  • To address the growing need for updated guidelines reflecting the latest medical trends in pediatric cardiology.
  • To provide a framework for managing the increasing adult population with Fontan circulation.

Main Methods:

  • Formation of a Korean Fontan cohort in 2019 and a guideline development committee in 2023.
  • Review and discussion of methodology and content by 19 working committee members with expert consultation.
  • Incorporation of international guidelines (US, Europe, Australia), Korean-specific data, survey data from the Korean Pediatric Cardiology Society, and meta-analysis results.

Main Results:

  • Development of the first Korean clinical practice guidelines for Fontan patients.
  • Inclusion of evaluations of international clinical guidelines.
  • Proposal of outpatient follow-up schedules specifically tailored to the Korean clinical context.
  • Rigorous review by leading national experts to ensure completeness and applicability.

Conclusions:

  • The newly developed Korean clinical practice guidelines provide comprehensive, context-specific recommendations for Fontan patient management.
  • These guidelines reflect the latest advancements in pediatric cardiology and address the unique needs of the Korean healthcare system.
  • The guidelines aim to enhance the long-term care and outcomes for adult Fontan circulation patients in Korea.

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