Early pacing in a child with Lodder-Merla syndrome and progressive sinus node dysfunction: a case report
Ahmed J AlAraibi1, Fatema Naser Shakeeb1, Aditya Bhat2
1School of Medicine, The Royal College of Surgeons in Ireland, Medical University of Bahrain, Busaiteen P.O. Box 15503, Bahrain.
European Heart Journal. Case Reports
|February 27, 2026
Summary
Lodder-Merla syndrome, a rare genetic disorder, can cause progressive sinus node dysfunction (SND). Early recognition and pacemaker implantation stabilized a young boy
Area of Science:
- Genetics
- Cardiology
- Neurology
Background:
- Lodder-Merla syndrome is a rare autosomal recessive disorder.
- Cardiac manifestations, such as progressive sinus node dysfunction (SND), can occur.
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