Severe mitral stenosis due to primary cardiac intimal sarcoma: case report
Jung-In Choi1, Jocelyn Y Chai1, Reed Huber2
1Division of Cardiology, Department of Medicine, and Centre for Cardiovascular Innovation, Vancouver General Hospital, University of British Columbia, 899 West 12th Avenue, Vancouver, BC V5Z 1N1, Canada.
European Heart Journal. Case Reports
|March 20, 2026
Summary
Primary cardiac intimal sarcomas are rare, aggressive tumors. This case highlights the challenges in diagnosis and treatment, emphasizing the need for multidisciplinary care for better patient outcomes.
Area of Science:
- Cardiovascular Pathology
- Oncology
- Surgical Oncology
Background:
- Primary cardiac tumors are rare, with intimal sarcomas being the rarest malignant subtype.
- Intimal sarcomas present late, causing hemodynamic compromise and having a poor prognosis due to rapid progression and metastasis.
- Multimodal management is crucial for intimal sarcomas due to a lack of standardized treatment guidelines.
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