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Updated: Mar 27, 2026

Chronic Thromboembolic Pulmonary Hypertension and Assessment of Right Ventricular Function in the Piglet
Published on: November 4, 2015
Recurrent systemic thromboembolism in paediatric restrictive cardiomyopathy: a case highlighting the need for early
Hakan Kurt1, Zulal Ulger1, Tülay Öztürk2
1Pediatric Cardiology, Ege Universityhttps://ror.org/02eaafc18, Türkiye.
Abstract:
Restrictive cardiomyopathy is a rare paediatric myocardial disorder causing diastolic dysfunction with preserved systolic function. We report a 14-year-old girl with idiopathic restrictive cardiomyopathy and recurrent systemic thromboemboli (stroke, limb ischaemia, renal infarction, and intracardiac thrombi) despite sinus rhythm. Anticoagulation resolved thrombi. She is currently awaiting heart transplantation. Early recognition, prompt anticoagulation, genetic evaluation, and consideration for transplantation are essential to optimise outcomes.
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