Proposed Standardized Nomenclature for Anomalous Aortic Origin of a Coronary Artery: An International
Carlos M Mery1, Meena Nathan2, Christoph Gräni3
1Pediatric Heart Institute, Monroe Carell Jr. Children's Hospital at Vanderbilt, Nashville, Tennessee, USA; Department of Cardiac Surgery, Vanderbilt University Medical Center, Nashville, Tennessee, USA.
Insights
A new standardized nomenclature for anomalous aortic origin of a coronary artery (AAOCA) has been proposed. This aims to unify descriptions, aiding risk stratification and evidence-based management of this congenital heart condition.
Area of Science:
- Cardiology
- Medical Imaging
- Congenital Heart Disease
Background:
- Advanced noninvasive imaging enhances characterization of congenital coronary artery anomalies.
- Anomalous aortic origin of a coronary artery (AAOCA) can cause myocardial ischemia with diverse clinical presentations.
- Current management is complicated by varied anatomic descriptions and lack of uniform nomenclature for high-risk features.
Purpose of the Study:
- To propose a standardized nomenclature for describing the anatomy and morphology of AAOCA.
- To unify descriptors within the scientific community for better communication.
- To facilitate the identification of high-risk features and improve risk stratification.
Main Methods:
- Utilized the Delphi methodology.
- Involved a group of experts in coronary artery anomalies (International Coronary Artery Anomalies Collaborative - ICAAC).
- Focused on developing a risk-agnostic system for describing AAOCA.
Main Results:
- A standardized nomenclature for AAOCA anatomy and morphology has been proposed.
- The system aims for uniformity in descriptors, irrespective of risk.
- Facilitates a common language for scientific discourse.
Conclusions:
- A unified nomenclature is crucial for describing AAOCA.
- Standardization will enable better definition of high-risk morphologic features.
- This will foster collaborative research and improve evidence-based management of AAOCA across all age groups.
Abstract:
Increasing use of advanced noninvasive imaging has provided great anatomic and morphologic details to characterize congenital coronary artery anomalies. Anomalous aortic origin of a coronary artery (AAOCA) is a subtype that may lead to myocardial ischemia with variable clinical manifestations across the lifespan. Management decision making in AAOCA is hindered by anatomic variants of differing physiologic consequences. Several systems of nomenclature have been used that lack uniformity in potentially high-risk morphologic features. The ICAAC (International Coronary Artery Anomalies Collaborative), a group of experts in coronary artery anomalies, proposes a standardized nomenclature to describe anatomy and morphologic features of AAOCA using the Delphi methodology. This system is agnostic of risk and intended to unify the descriptors of AAOCA within the scientific community. A common language will allow definition of high-risk morphologic features inducing myocardial ischemia while fostering collaborative efforts to improve risk stratification in AAOCA across ages, ultimately guiding evidence-based management decision making.
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