Prophylactic resection of an incidental right ventricular fibroma in a child

Area of Science:

• Pediatric Cardiology
• Cardiac Oncology
• Surgical Oncology

Background:

• Cardiac fibromas are rare, benign tumors typically found in children.
• These tumors can be incidentally discovered during routine examinations.
• While often asymptomatic, they pose risks such as arrhythmias.

Purpose of the Study:

• To present a case of an asymptomatic pediatric cardiac fibroma.
• To discuss the rationale and outcomes of prophylactic surgical intervention.
• To emphasize the importance of early detection and management in pediatric cardiac tumors.

Main Methods:

• A 4-year-old asymptomatic boy with a right ventricular fibroma.
• Diagnosis confirmed via echocardiography and cardiac computed tomography.
• Prophylactic complete tumor resection performed.
• Histopathological analysis to confirm fibroma.

Main Results:

• A 24.5 × 33.6 mm well-circumscribed mass was identified in the right ventricular outflow tract.
• The patient experienced no hemodynamic compromise.
• Post-surgery, the patient remained recurrence-free with normal ventricular function at 8-year follow-up.

Conclusions:

• Early surgical intervention for pediatric cardiac fibromas is recommended, even in asymptomatic cases.
• Prophylactic resection mitigates risks associated with non-regressive and potentially arrhythmogenic tumors.
• Timely management ensures favorable long-term outcomes and prevents serious cardiac events.