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Interventional Diagnostic Procedure: A Practical Guide for the Assessment of Coronary Vascular Function
Published on: March 15, 2022
Current evidence for diagnosis and management of cardiac vasculitis
Shaun Khanna1,2,3, Aditya Bhat4,5, Liza Thomas2,4
1Cardiovascular Program, The George Institute for Global Health, Sydney, New South Wales, Australia shaunkhanna@hotmail.com.
Insights
Cardiac vasculitis, a rare immune disorder affecting the heart, presents diagnostic challenges due to non-specific symptoms. Early recognition and advanced imaging are key for timely treatment and improved outcomes in cardiovascular conditions.
Area of Science:
- Cardiology
- Rheumatology
- Immunology
Background:
- Cardiac vasculitis is a rare, immune-mediated condition affecting heart structures.
- It can lead to severe cardiac events like acute coronary syndrome and heart failure.
- Non-specific symptoms often delay diagnosis, complicating management.
Purpose of the Study:
- To highlight the challenges in diagnosing cardiac vasculitis.
- To discuss advances in imaging and collaborative care for recognition and management.
- To outline current treatment recommendations and future research needs.
Main Methods:
- Review of current literature on cardiac vasculitis diagnosis and management.
- Discussion of advanced non-invasive imaging techniques (PET-MRI, CT).
- Emphasis on European Alliance of Associations for Rheumatology (EULAR) treatment guidelines.
Main Results:
- Cardiac vasculitis diagnosis is challenging due to overlapping symptoms with other cardiovascular diseases.
- Multimodality imaging and cardio-rheumatology collaboration improve recognition.
- Early immunosuppression and cardiovascular risk management are recommended treatments.
Conclusions:
- Advances in imaging and integrated care enhance cardiac vasculitis recognition.
- Intensive immunosuppression and risk management are crucial for remission.
- Further research is needed for imaging-guided algorithms and long-term outcomes.
Abstract:
Cardiac vasculitis represents a heterogeneous group of immune-mediated disorders that can involve the coronary vessels, myocardium, valvular apparatus and pericardial tissues. Despite its rarity, cardiac vasculitis may result in significant clinical sequelae such as acute coronary syndrome, heart failure, cardiac arrhythmias and pericarditis. Diagnosis is challenging because symptoms are often non-specific and overlap with other cardiovascular conditions. Early recognition is therefore crucial to prevent delayed treatment and disease progression. Advances in non-invasive multimodality imaging and collaborative cardio-rheumatology care have transformed recognition and management of this disease spectrum. Emerging techniques such as hybrid positron emission tomography-cardiac MRI and quantitative CT imaging permit in-vivo characterisation of inflammation. As per European Alliance of Associations for Rheumatology recommendations, treatment requires early intensive immunosuppression to induce remission, coupled with comprehensive cardiovascular risk management. Additional research is required to validate imaging-guided management algorithms, refine vasculitis-specific cardiovascular risk and define long-term outcomes across disease subtypes.
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