Adult Supracardiac Total Anomalous Pulmonary Venous Connection: An Uncommon Entity

Total anomalous pulmonary venous connection (TAPVC), a congenital cardiac disorder, usually manifests in early infancy. Its presentation may be catastrophic if the drainage site into the systemic venous circulation is obstructed. Conversely, in the absence of such obstruction, its presentation may be delayed. Very few sporadic case reports or small series describing its presentation in adult patients are available. In this report, we present an adult patient with this diagnosis, in whom all four pulmonary veins had joined to form a common pulmonary venous confluence (CPVC) that drained into a left vertical vein, which in turn drained into the innominate vein.