Related Experiment Video
Updated: May 4, 2026
04:41
Application of the En Bloc Concept Combined with Anatomic Resection in Laparoscopic Hepatectomy
Published on: March 10, 2023
1.9K
Laparoscopic partial hepatectomy for primary hepatic PEComa: a case report
Bing Liang1,2, Hongjin Shi3, Qingbin Zeng1
1Department of Hepatopancreatobiliary Surgery, The Second Affiliated Hospital of Kunming Medical University, No. 374 Dianmian Road, Kunming, Yunnan, 650101, China.
BMC Gastroenterology
|May 2, 2026
Summary
Perivascular epithelioid cell tumors (PEComas) are rare liver tumors. This case highlights diagnostic challenges and successful surgical management of a large hepatic PEComa in a young male patient.
Area of Science:
- Oncology
- Pathology
- Surgical Gastroenterology
Background:
- Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal neoplasms.
- PEComas exhibit dual differentiation of smooth muscle cells and melanocytes.
- Diagnosis is challenging due to nonspecific symptoms and imaging findings.
Purpose of the Study:
- To present a case of a large hepatic PEComa in a young male.
- To detail the diagnostic process, including imaging characteristics.
- To describe the surgical management and outcomes for hepatic PEComa.
Main Methods:
- A 31-year-old male presented with an incidentally discovered hepatic lesion.
- Comprehensive imaging (ultrasound, CT, MRI) was performed.
- Laparoscopic partial hepatectomy was conducted, followed by histopathological analysis.
Main Results:
- Imaging suggested hepatocellular carcinoma, necessitating differential diagnosis.
- Histopathology confirmed a PEComa with undetermined malignant potential.
- The patient experienced an uneventful recovery and was discharged.
Conclusions:
- PEComas are rare with insidious onset and challenging early diagnosis.
- Imaging findings are often nonspecific, with biopsy crucial for diagnosis.
- Radical resection (R0) is the definitive treatment for PEComa.
