Anesthetic Considerations in Sturge-Weber Syndrome: A Case Report
Neslida Kodra1, Karina Escalona1, Peter Hsin2
1Anesthesiology, Mount Sinai Medical Center, Miami Beach, USA.
Cureus
|May 4, 2026
Summary
Anesthetic management for Sturge-Weber syndrome (SWS) requires careful planning for difficult airways and seizure control. This case report details successful dental surgery under general anesthesia for an SWS patient, emphasizing airway and hemorrhage risk mitigation.
Area of Science:
- Anesthesiology
- Neurology
- Genetics
Background:
- Sturge-Weber syndrome (SWS) is a rare congenital neurocutaneous disorder.
- It presents significant anesthetic challenges due to extensive vascular malformations, particularly facial and oral angiomas.
- Key concerns include difficult airway management, seizure control, and maintaining intracranial and intraocular pressures.
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