A Case of Occipitocervical Fixation for Orthotopic Os Odontoideum in a 2-year-old Child with Progressive Floppy

Yosuke Hashimoto1, Hisaaki Uchikado1,2, Takehiro Makizono1

  • 1Department of Neurosurgery, Kurume University School of Medicine, Asahi-machi, Kurume, Japan.

Insights

Craniocervical instability in infants, a rare cause of floppy infant syndrome, presents significant treatment challenges. Surgical intervention halted progressive paralysis in a 2-year-old diagnosed with orthotopic os odontoideum.

Area of Science:

  • Pediatric Neurology
  • Neurosurgery
  • Developmental Pediatrics

Background:

  • Craniocervical instability is a rare cause of infantile hypotonia (floppy infant syndrome).
  • Treatment is complicated by underdeveloped bone structures in infants.
  • Progressive neurological decline can occur if left untreated.

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