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Concomitant Budd-Chiari syndrome and coronary artery pseudoaneurysm in Behçet's disease: A case report

Jianing Chen1, Hao Zhu1, Yuansheng Xu1

  • 1The Second Hospital & Clinical Medical School, Lanzhou University, No. 82, Cuiying Gate, Chengguan District 730030, Lanzhou, China.

The International Journal of Cardiovascular Imaging
|May 26, 2026
PubMed

Insights

Behçet

Area of Science:

  • Cardiology
  • Rheumatology
  • Vascular Medicine

Background:

  • Behçet's disease (BD) is a rare multisystem vasculitis.
  • Budd-Chiari syndrome (BCS) is a severe manifestation of BD, while coronary involvement is uncommon.
  • Concomitant BCS and coronary pseudoaneurysm in BD is exceptionally rare.

Purpose of the Study:

  • To report a rare case of concomitant Budd-Chiari syndrome and coronary pseudoaneurysm in a young patient with Behçet's disease.
  • To highlight the importance of considering BD in young patients with unexplained myocardial infarction and venous thrombosis.
  • To emphasize the role of multimodality cardiovascular imaging in diagnosis and management.

Main Methods:

  • Case report of a 23-year-old male with BCS presenting with acute chest pain.
  • Diagnostic workup included transthoracic echocardiography, contrast-enhanced CT, and coronary angiography.
  • Percutaneous coronary intervention with stent implantation was performed for LAD pseudoaneurysm.

Main Results:

  • The patient presented with severe LV dysfunction and a left anterior descending artery (LAD) pseudoaneurysm.
  • Coronary angiography confirmed LAD stenosis and pseudoaneurysm, treated successfully with stenting.
  • Diagnosis of Behçet's disease was confirmed based on clinical criteria and treated with immunosuppressants, leading to improvement.

Conclusions:

  • Young patients with myocardial infarction and no traditional risk factors, especially with BCS or venous thrombosis, should be evaluated for Behçet's disease.
  • Multimodality cardiovascular imaging is crucial for diagnosing vascular Behçet's disease and guiding treatment.
  • Early diagnosis and immunosuppressive therapy are vital for favorable outcomes in vascular Behçet's disease.

Keywords:
Behçet’s diseaseBudd–Chiari syndromeCoronary artery pseudoaneurysmMultimodality imagingPercutaneous coronary intervention

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