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Published on: February 11, 2022
[Incidental diagnosis of cor triatriatum sinister in a young woman]
Rita Cristina Myriam Intravaia1, Michele Massimo Gulizia1
1U.O.C. Cardiologia con UTIC, Azienda di Rilievo Nazionale e Alta Specializzazione "Garibaldi", P.O. "Garibaldi-Nesima", Catania.
Insights
Cor triatriatum sinister (CTS) is a rare congenital heart defect where a membrane divides the left atrium. Echocardiography is key for diagnosing CTS in adults and guiding management, even in asymptomatic cases.
Area of Science:
- Cardiology
- Congenital Heart Disease
- Cardiac Imaging
Background:
- Cor triatriatum sinister (CTS) is a rare congenital heart defect, affecting 0.1-0.4% of cases.
- It is characterized by a fibromuscular septum dividing the left atrium into two chambers.
- Diagnosis in adulthood is uncommon, often incidental.
Purpose of the Study:
- To report a case of incidentally diagnosed Cor triatriatum sinister in a 37-year-old woman.
- To highlight the role of echocardiography in diagnosis and risk stratification.
- To discuss the management of asymptomatic CTS in adults.
Main Methods:
- Transthoracic echocardiography (TTE) for initial assessment.
- Transesophageal echocardiography (TEE) for detailed characterization.
- Classification using the Loeffler criteria.
Main Results:
- Incidental diagnosis of CTS in a 37-year-old woman presenting with chest pain.
- TTE revealed a left intra-atrial membrane; TEE confirmed no significant hemodynamic impact.
- Patient classified as Loeffler group III due to membrane patency and non-significant gradient.
- No significant associated cardiac anomalies were identified.
Conclusions:
- Echocardiography is crucial for diagnosing and assessing the hemodynamic significance of CTS in adults.
- Asymptomatic patients with non-obstructive CTS generally have a favorable prognosis.
- Long-term arrhythmia monitoring is recommended due to risks of atrial fibrillation and cardioembolic events.
Abstract:
Cor triatriatum sinister (CTS) is a rare congenital heart defect, with an estimated incidence of 0.1-0.4% of all congenital heart defects, characterized by the presence of a fibromuscular septum that divides the left atrium into two chambers. We report the case of a 37-year-old woman with an incidental diagnosis of CTS during hospitalization for chest pain. Transthoracic echocardiography revealed a left intra-atrial membrane without hemodynamic significance, subsequently better characterized by transesophageal echocardiography, which ruled out the presence of a significant gradient and associated cardiac anomalies, including atrial septal defects. The patient was classified in Loeffler group III due to the presence of extensive patency of the membrane associated with a non-significant transmembrane gradient. In the absence of hemodynamically significant obstruction and associated congenital heart disease, the natural history is generally favorable. In asymptomatic patients, a conservative approach is adopted, involving clinical and instrumental follow-up and control of risk factors. However, in light of the risk of atrial fibrillation and cardioembolic events, long-term arrhythmia monitoring is indicated. This case highlights the role of echocardiographic imaging in the diagnosis and risk stratification of CTS in adults.
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