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Congenital microtia-atresia in Iran: a case report
Mahsa Shiravani1, Marzyeh Alipour2, Ahmad Reza Mortajez3
1Department of Midwifery, Obstetrics and Gynecology, Vali-E-Asr Hospital, Kazerun, Iran.
Journal of Medical Case Reports
|July 4, 2026
Summary
This case report details a rare instance of isolated unilateral microtia-atresia in a newborn. Early identification is vital for timely hearing assessments and management of this congenital ear anomaly.
Area of Science:
- Medical Case Reports
- Pediatric Congenital Anomalies
- Otolaryngology
Background:
- Microtia-atresia is a rare congenital condition affecting external ear development.
- Incidence ranges from 3 to 10 per 10,000 live births, often unilateral and affecting the right ear.
- Both genetic and environmental factors are implicated in its etiology.
Purpose of the Study:
- To report a rare case of isolated unilateral microtia with aural atresia.
- To highlight the importance of early recognition and management in newborns.
- To contribute to understanding the clinical variability of microtia.
Main Methods:
- Presentation of a term female infant with isolated right microtia-atresia.
- Clinical examination findings, noting absence of other craniofacial abnormalities.
- Review of relevant literature on microtia-atresia.
Main Results:
- The infant presented with isolated unilateral microtia-atresia without syndromic features.
- No other congenital anomalies were identified.
- The case underscores the spectrum of microtia presentation.
Conclusions:
- Isolated unilateral microtia-atresia is a rare presentation requiring prompt evaluation.
- Early intervention is crucial for optimal hearing and developmental outcomes.
- Case reports aid in understanding the diverse clinical landscape of microtia.
