Developmental Systems Cardiology: A Longitudinal Adaptive Framework for Congenital Heart Disease

Colin J McMahon1,2, Jeffrey Kim3, Mark Lewin4

  • 1Department of Pediatric Cardiology, Children's Health Ireland at Crumlin, Dublin 12, Ireland. cmcmahon992004@yahoo.com.

Insights

Congenital heart disease (CHD) care now requires a lifelong approach, focusing on adaptation and support systems beyond survival. Developmental Systems Cardiology (DSC) offers a framework for integrated, lifelong care for children and families navigating CHD challenges.

Area of Science:

  • Pediatric Cardiology
  • Developmental Pediatrics
  • Health Systems Science

Background:

  • Survival rates for congenital heart disease (CHD) have improved significantly due to medical advancements.
  • Contemporary challenges in CHD extend beyond procedural success, encompassing neurodevelopmental, psychosocial, and lifelong adaptation needs.
  • Social determinants of health and healthcare access significantly influence long-term CHD outcomes.

Purpose of the Study:

  • To introduce Developmental Systems Cardiology (DSC) as an integrative framework for lifelong CHD care.
  • To explore how DSC can inform various aspects of care, including neurodevelopmental support, psychosocial care, and healthcare transitions.
  • To emphasize adaptation as a key outcome and organizing principle in managing CHD across the lifespan.

Main Methods:

  • Conceptual framework development: Developmental Systems Cardiology (DSC).
  • Literature synthesis on challenges and influences in lifelong CHD care.
  • Exploration of DSC's application to clinical practice, implementation science, and professional formation.

Main Results:

  • DSC conceptualizes CHD as a lifelong adaptive process influenced by biological, developmental, psychosocial, community, and healthcare factors.
  • The framework highlights the impact of organizational factors, implementation, and health inequities on long-term outcomes.
  • DSC provides a model for enhancing neurodevelopmental surveillance, psychosocial support, and coordinated transition medicine.

Conclusions:

  • Future progress in CHD requires strengthening developmental, relational, educational, community, and organizational support systems.
  • Adaptation is proposed as a central clinical outcome and implementation target within the DSC framework.
  • DSC promotes integrated, lifespan care for individuals with CHD, particularly those with complex conditions like Fontan circulation.

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