Pericardiectomy for constrictive pericarditis in a cystic fibrosis patient

Arouba Imtiaz1, Syed Nong-Chek2, Indu Deglurkar2

  • 1All Wales Adult Cystic Fibrosis Centre, University Hospital Llandough, Llandough, UK arouba.imtiaz@nhs.net.

BMJ Case Reports
|July 17, 2026
PubMed

Insights

Complication rates are rising in ageing cystic fibrosis (CF) patients. This case report details the first instance of constrictive pericarditis in a CF patient with end-stage renal disease (ESRD) requiring hemodialysis, successfully treated with pericardiectomy.

Area of Science:

  • Nephrology
  • Cardiology
  • Pulmonology

Background:

  • Ageing cystic fibrosis (CF) populations experience increasing complication rates.
  • CF-related diabetes is linked to microvascular complications, including end-stage renal disease (ESRD).
  • Patients undergoing hemodialysis have a higher incidence of pericarditis.

Purpose of the Study:

  • To report the first case of constrictive pericarditis in a cystic fibrosis patient with ESRD.
  • To highlight the link between ESRD, hemodialysis, and pericarditis in CF patients.
  • To document the successful treatment of this condition with pericardiectomy.

Main Methods:

  • Case report.
  • Review of patient history and treatment.
  • Surgical intervention (pericardiectomy).

Main Results:

  • A cystic fibrosis patient with ESRD requiring hemodialysis developed constrictive pericarditis.
  • The patient underwent successful pericardiectomy.
  • This represents the first documented case of its kind.

Conclusions:

  • Constrictive pericarditis is a potential complication in ageing CF patients with ESRD undergoing hemodialysis.
  • Pericardiectomy can be an effective treatment for this specific complication.
  • Increased vigilance for cardiac complications in this patient group is warranted.

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