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Clinical and Laboratory Transition Between GPA and EGPA
Sergey V Fedosenko1, Mats Junek1, Carmen Venegas Garrido1
1Divisions of Respirology and Rheumatology, McMaster University and St Joseph's Healthcare, Hamilton, ON, Canada.
Chest
|August 10, 2026
Summary
Antineutrophil cytoplasmic antibody-associated vasculitis (AAV) subtypes like Granulomatosis with polyangiitis (GPA) and Eosinophilic granulomatosis with polyangiitis (EGPA) can transition between phenotypes. Recognizing these dynamic changes is crucial for accurate AAV diagnosis and treatment.
Area of Science:
- Rheumatology
- Immunology
- Pulmonology
Background:
- Granulomatosis with polyangiitis (GPA) and Eosinophilic granulomatosis with polyangiitis (EGPA) are distinct antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV) subtypes.
- The clinical distinctions between GPA and EGPA may not always be rigid, suggesting potential for phenotype transitions.