Precision minimally invasive strategy for Hirschsprung's disease: from anatomical resection to whole-cycle functional

Kai Zheng1, Wenyue Ma1, Rui Li1

  • 1Department of Pediatric Surgery, Tianjin Medical University General Hospital, Tianjin, TJ, China.

Frontiers in Pediatrics
|August 14, 2026
PubMed

Insights

Minimally invasive surgery for Hirschsprung disease (HD) improves outcomes, but functional management is key. This review proposes a holistic, function-oriented framework for better pediatric patient quality of life.

Area of Science:

  • Pediatric Surgery
  • Gastroenterology
  • Clinical Management

Background:

  • Minimally invasive surgery for Hirschsprung disease (HD) has advanced accuracy and safety.
  • Postoperative defecation dysfunction remains a significant challenge impacting pediatric patients' quality of life.
  • Current reviews often lack a comprehensive, whole-cycle functional management approach for HD.

Purpose of the Study:

  • To review precision minimally invasive surgical strategies for Hirschsprung disease.
  • To propose an integrated, whole-cycle functional management framework for HD patients.

Main Methods:

  • Systematic literature search across major databases (PubMed, Scopus, etc.).
  • Inclusion of studies on minimally invasive surgery, defecation function, and management strategies for HD.
  • Exclusion of non-English literature and conference abstracts without full text.

Main Results:

  • Summarized current precision minimally invasive therapeutic strategies for Hirschsprung disease.
  • Analyzed the comprehensive care pathway for HD.
  • Identified a shift towards holistic, function-oriented management.

Conclusions:

  • A paradigm shift from isolated anatomical resection to function-oriented management is crucial for HD.
  • Implementing a whole-cycle functional management framework can improve long-term outcomes for pediatric HD patients.
  • Precision minimally invasive techniques combined with holistic care offer improved quality of life.
Abstract