Isolated Congenital Ossicular Chain Anomalies

Natsuko Obara1, Hiroshi Okuda1, Noriko Nagase1

  • 1Otolaryngology-Head and Neck Surgery, Gifu University Graduate School of Medicine, Gifu, JPN.

Cureus
|August 14, 2026
PubMed
Summary

Congenital ossicular chain anomalies (COCAs) can run in families, causing conductive hearing loss even with normal ear exams. Early imaging and surgery can significantly improve hearing in affected siblings.