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Updated: Sep 5, 2026

Forskolin-induced Swelling in Intestinal Organoids: An In Vitro Assay for Assessing Drug Response in Cystic Fibrosis Patients
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CFTR Modulator Therapy and Aerobic Fitness Changes in Aerobic Fitness Following Initiation of CFTR Modulator Therapy:

Ingrid Silveira de Almeida1, Fernanda Maria Vendrusculo1, Mariana Severo da Costa1

  • 1Laboratory of Physical Activity in Pediatrics, Centro Infant, Pontifícia Universidade Católica do Rio Grande do Sul (PUCRS), Porto Alegre, Rio Grande do Sul, Brazil.

Pediatric Pulmonology
|September 3, 2026
PubMed
Abstract

Keywords:
CFTR modulator therapy, cardiopulmonary exercise testingaerobic fitnesscystic fibrosisoxygen consumption

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