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Unilateral Scotoma as Inaugural Sign in Moyamoya Disease
Deborah A Lipski1, Simon-Pierre Docquier2, Florence Rasquin1
1Department of Ophthalmology, HUB Erasme Hospital, Université Libre de Bruxelles.
Purpose:
To report a case of Moyamoya Disease presenting with unilateral scotoma caused by unilateral sectorial optic nerve atrophy, associated with macular microaneurysms.
Methods:
Observational case report.
Results:
A 38-year-old patient presented with unilateral scotoma in his right eye. Optic nerve atrophy in the corresponding sector was observed, as well as unilateral macular microaneurysms and peri-foveal capillary dropout. Brain magnetic resonance imaging, magnetic resonance angiography and conventional angiography showed supra-clinoid, anterior, middle, and posterior cerebral Moyamoya disease, with vascular clutter around the right optic canal. Relative stenosis of the left cavernous carotid artery was also present.
Conclusion:
This report describes a patient whose inaugural sign of Moyamoya Disease was unilateral scotoma, that was associated with macular vascular malformations.
