Amaurosis fugax associated with SC hemoglobinopathy and lupus erythematosus

A 23-year-old woman with SC hemoglobinopathy and systemic lupus erythematosus had recurrent amaurosis fugax in her right eye. Extraordinary retinal vascular events were observed and photographed during the amaurotic attacks. Prednisone therapy halted the attacks. We believe a focal lupus vasculopathy involving the central retinal artery caused the amaurosis fugax.