Unilateral, linear, zosteriform epidermal nevus with acantholytic dyskeratosis

An infant has a nevus unius lateris with the histopathologic condition of acantholytic dyskeratosis. Similar cases have, in the past, been classified as unilateral Darier's disease. Since it is now recognized that the pathologic changes of acantholytic dyskeratosis are not specific for a given disease entity, we believe the concept of unilateral keratosis follicularis deserves reevaluation.