Double outlet from chambers of left ventricular morphology

Area of Science:

• Cardiology
• Congenital Heart Disease
• Pediatric Cardiology

Background:

• Double outlet of the left ventricle (DOLV) is a complex congenital heart anomaly.
• Accurate diagnosis and understanding of associated defects are critical for patient management.

Purpose of the Study:

• To report a series of 5 cases with double outlet of the left ventricle.
• To highlight diagnostic challenges and the importance of detailed anatomical assessment for surgical planning.

Main Methods:

• Review of 1700 heart specimens to determine incidence.
• Analysis of one surgically corrected case.
• Discussion of diagnostic modalities, including axial cineangiography.

Main Results:

• An incidence of 0.23% for DOLV was identified in the reviewed specimens.
• Four of the five cases had abnormal atrioventricular connections precluding total correction.
• Frequent findings included absence of the infundibular septum and aortic laevoposition.

Conclusions:

• Clinical diagnosis of DOLV can be challenging.
• Axial cineangiography may aid in anatomical diagnosis.
• Detailed assessment of ventricular size, atrioventricular valves, VSD, and outflow tract obstruction is essential for surgical consideration.